Plexiform neurofibroma of uterus: a rare manifestation of neurofibromatosis 1.
نویسندگان
چکیده
Neurofibromatosis type 1 (NF1) rarely affects the female genital system. Plexiform neurofibromas are congenital lesions that occur exclusively in patients with neurofibromatosis type I. The vulva is the most frequent genital organ to be affected, whereas vaginal, cervical, uterine, and ovarian neurofibromas have also been reported only rarely. We present an 8 years old girl with plexiform neurofibroma primarily involving genital system.
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عنوان ژورنال:
- Journal of the College of Physicians and Surgeons--Pakistan : JCPSP
دوره 24 Suppl 1 شماره
صفحات -
تاریخ انتشار 2014